Relevant publications:
- Lentiviral-Mediated Phenotypic Correction of Cystic Fibrosis Pigs. Cooney AL, Abou Alaiwa MH, Shah VS, Bouzek DC, Stroik MR, Powers LS, Gansemer ND, Meyerholz DK, Welsh MJ, Stoltz DA, Sinn PL, McCray PB Jr. JCI Insight, 2016;1(14):e88730. doi:10.1172/jci.insight.88730.
- Airway Acidification Initiates Host Defense Abnormalities in Cystic Fibrosis Mice. Shah VS, Meyerholz DK, Tang XX,Reznikov L, Abou Alaiwa M, Ernst SE, Karp PH, Wohlford-Lenane CL, Heilmann KP, Leidinger MR, Allen PD, Zabner J, McCray PB Jr, Ostedgaard LS, Stoltz DA, Randak CO, and Welsh MJ. Science, 351(6272):503-507, 2016. PMCID: PMC4852973.
- Lentiviral-Mediated Phenotypic Correction of Cystic Fibrosis Pigs. Cooney AL, Abou Alaiwa MH, Shah VS, Bouzek DC, Stroik MR, Powers LS, Gansemer ND, Meyerholz DK, Welsh MJ, Stoltz DA, Sinn PL, McCray PB Jr. JCI Insight, 2016;1(14):e88730. doi:10.1172/jci.insight.88730.
- Newborn Cystic Fibrosis Pigs Have a Blunted Early Response to an Inflammatory Stimulus. Bartlett JA, Ramachandran S, Wohlford-Lenane CL, Barker CK, Pezzulo AA, Zabner J, Welsh MJ, Meyerholz DK, Stoltz DA, McCray PB Jr. Am J Respir Crit Care Med. 2016. Mar 30. [Epub ahead of print] PMID: 27027566
- Glandular Proteome Identifies Antiprotease Cystatin C as a Critical Modulator of Airway Hydration and Clearance. Evans, TI, Joo, NS, Keiser, NW, Yan, Z, Tyler, SR, Xie, W, Zhang, Y., Hsiao, JJ, Cho, HJ, Wright, ME, Wine, JJ, and Engelhardt, JF 2015. Am J Respir Cell Mol Biol. (In Press)
- Ferret and Pig Models of Cystic Fibrosis: Prospects and Promise for Gene Therapy. Yan Z, Stewart ZA, Sinn PL, Olsen JC, Hu J, McCray PB Jr, Engelhardt JF. Hum Gene Ther Clin Dev 2015. Mar;26(1):38-49. doi: 10.1089/humc.2014.154. Epub 2015 Feb 12. PMID: 25675143.
- Sox2 Modulates Lef-1 Expression During Airway Submucosal Gland Development. Xie, W, Lynch, TJ, Liu, X, Tyler, SR, Yu, S, Zhou, X, Luo, M, Kusner, DM, Sun, X, Yi, Y, Zhang, Y, Goodheart, MJ, Parekh, KR, Wells, JM, Xue, HH, Pevny, LH, and Engelhardt, JF 2014. Am J Physiol Lung Cell Mol Physiol 306:L645-660. PMCID:3962629.
- Neonates with Cystic Fibrosis Have a Reduced Nasal Liquid pH; A Small Pilot Study. Abou Alaiwa MH, Beer AM, Pezzulo AA, Launspach JL, Horan RA, Stoltz DA, Starner TD, Welsh MJ, Zabner J. J Cyst Fibros. 2014 Jul;13(4):373-7.doi:10.1016/j.jcf.2013.12.006. Epub 2014 Jan 11. PubMed PMID: 24418186; PubMed Central PMCID: PMC4060428.